Coenzyme Q9
货号：
16866-500ug 基本售价：
406.0 元 规格：
500 ug
产品信息
概述| 货号 | 16866-500ug |
| 描述 | Coenzyme Q9(CoQ9) is a nine isoprenyl group-containing member of the mitochondrial ubiquinone family that is thought to be necessary for the biosynthesis of CoQ10 (Item No. 11506) in humans. Mutations in the gene that encodes CoQ9 are associated with encephalomyopathy and autosomal-recessive, neonatal-onset, primary CoQ10deficiency.1,2 While in humans CoQ10 predominates, mice and C. elegans primarily rely on CoQ9 for electron transport through the mitochondrial respiratory chain and for antioxidant functions.3 |
| 别名 | CoQ9;NSC 226993;Ubiquinone-9;Ubiquinone Q9; |
性能| 供应商 | Cayman |
| 应用文献 |
1.Duncan, A.J.,Bitner-Glindzicz, M.,Meunier, B., et al. A nonsense mutation in COQ9 causes autosomal-recessive neonatal-onset primary coenzyme Q10 deficiency: A potentially treatable form of mitochondrial disease. American Journal of Human Genetics 84(5), 558-566 (2009).
2.García-Corzo, L.,Luna-Sánchez, M.,Doerrier, C., et al. Dysfunctional Coq9 protein causes predominant encephalomyopathy associated with CoQ deficiency. Human Molecular Genetics 22(6), 1233-1248 (2013).
3.Lapointe, J.,Wang, Y.,Bigras, E., et al. The submitochondrial distribution of ubiquinone affects respiration in long-lived Mclk1+/- mice. Journal of Cell Biology 199(2), 215-224 (2012).
|
| 运输条件 | Room temperature in continental US; may vary elsewhere |
| 存放说明 | -20 |
| 纯度 | ≥95% |
| 计算分子量 | 795.2 |
| 分子式 | C54H82O4 |
| CAS号 | 303-97-9 |
| 稳定性 | ≥ 2 years |
声明| 本官网所有报价均为常温或者蓝冰运输价格，如有产品需要干冰运输，需另外加收干冰运输费。 |
