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货号： bs-6643R-AF350 基本售价： 2980.0 元 规格： 100ul
产品信息
- 产品编号
- bs-6643R-AF350
- 英文名称
- Anti-SCYL1BP1/AF350
- 中文名称
- AF350标记的SCYL结合蛋白1抗体
- 别 名
- hNTKL BP1; N terminal kinase like binding protein 1; NTKL binding protein 1; NTKL BP1; NTKLBP 1; NTKLBP1; SCY1 like 1 binding protein 1; SCYL1 binding protein 1; SCYL1 BP1; GORAB_HUMAN.
- 规格价格
- 100ul/2980元购买 大包装/询价
- 说 明 书
- 100ul
- 研究领域
- 细胞生物 信号转导
- 抗体来源
- Rabbit
- 克隆类型
- Polyclonal
- 交叉反应
- Human, Mouse, Rat, Chicken, Dog, Pig, Cow, Horse, Rabbit,
- 产品应用
- IF=1:50-200
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
- 分 子 量
- 45kDa
- 性 状
- Lyophilized or Liquid
- 浓 度
- 1mg/ml
- 免 疫 原
- KLH conjugated synthetic peptide derived from human SCYL1BP1
- 亚 型
- IgG
- 纯化方法
- affinity purified by Protein A
- 储 存 液
- 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol
- 保存条件
- Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
- 产品介绍
- background:
Defects in GORAB are the cause of geroderma osteodysplasticum (GO) [MIM:231070]; also known as gerodermia osteodysplastica or Walt Disney dwarfism. GO is a rare autosomal recessive disorder characterized by lax, wrinkled skin, joint laxity and a typical face with a prematurely aged appearance. Skeletal signs include severe osteoporosis leading to frequent fractures, malar and mandibular hypoplasia and a variable degree of growth retardation.
Subunit:
Interacts with SCYL1 (By similarity). Interacts with RCHY1 and RAB6A/RAB6.
Subcellular Location:
Cytoplasm. Golgi apparatus.
DISEASE:
Defects in GORAB are the cause of geroderma osteodysplasticum (GO) [MIM:231070]; also known as gerodermia osteodysplastica or Walt Disney dwarfism. GO is a rare autosomal recessive disorder characterized by lax, wrinkled skin, joint laxity and a typical face with a prematurely aged appearance. Skeletal signs include severe osteoporosis leading to frequent fractures, malar and mandibular hypoplasia and a variable degree of growth retardation.
Similarity:
Belongs to the GORAB family.
Database links:
UniProtKB/Swiss-Prot: Q5T7V8.1
Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.