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货号： bs-15334R-PE-Cy7 基本售价： 2980.0 元 规格： 100ul
产品信息
- 产品编号
- bs-15334R-PE-Cy7
- 英文名称
- Anti-C9orf61/PE-Cy7
- 中文名称
- PE-Cy7标记的9号染色体开放阅读框61抗体
- 别 名
- Chromosome 9 open reading frame 61; Friedreich ataxia region gene X123; MGC142243; MGC142245; OTTHUMP00000063356; Protein X123; RP11 548B3.1; Uncharacterized protein C9orf61; X123; F1892_HUMAN.
- 规格价格
- 100ul/2980元购买 大包装/询价
- 说 明 书
- 100ul
- 研究领域
- 细胞生物 免疫学
- 抗体来源
- Rabbit
- 克隆类型
- Polyclonal
- 交叉反应
- Human,
- 产品应用
- ICC=1:50-200 IF=1:50-200
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
- 分 子 量
- 47kDa
- 性 状
- Lyophilized or Liquid
- 浓 度
- 1mg/ml
- 免 疫 原
- KLH conjugated synthetic peptide derived from human C9orf61
- 亚 型
- IgG
- 纯化方法
- affinity purified by Protein A
- 储 存 液
- 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
- 保存条件
- Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
- 产品介绍
- background:
Friedreichs ataxia is an inherited disease that is characterized by a progressive degeneration of the spinal cord and nerve tissue. Caused by a mutated gene region on chromosome 9 that results in mitochondrial malfunction, Friedreichs ataxia can lead to a variety of conditions including speech problems, vision impairment, muscle weakness, diabetes and scoliosis. X123, also known as C9orf61 (chromosome 9 open reading frame 61), is a 289 amino acid protein that is expressed at high levels in skeletal muscle and at lower levels in brain, heart and lung. The gene encoding X123 is located within the Friedreichs ataxia region on chromosome 9, suggesting a possible role for X123 in the pathogenesis of this disease.
Subcellular Location:
Membrane; Single-pass type I membrane protein (Potential).
Tissue Specificity:
Prominently expressed in muscle.
Similarity:
Belongs to the FAM189 family.
Database links:Entrez Gene: 9413Human
Omim: 607710Human
SwissProt: Q15884Human
Unigene: 118003Human
Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.