Mucolipin 1 Blocking Peptide - (Dry Ice)
货号：
NB110-82375PEP 基本售价：
1219.4 元 规格：
0.1 ml
产品信息
概述| 货号 | NB110-82375PEP |
| 反应种属 | MuSpecies Glossary |
性能| 供应商 | Novus |
| 背景 | Defects in Mucolipin-1 are the cause of mucolipidosis type IV (MLIV), also known as sialolipidosis. MLIV is an autosomal recessive lysosomal storage disorder characterized by severe psychomotor retardation and ophthalmologic abnormalities, including corneal opacity, retinal degeneration and strabismus. Storage bodies of lipids and water-soluble substances are seen by electron microscopy in almost every cell type of the patients. Most patients are unable to speak or walk independently and reach a maximal developmental level of 1-2 years. All patients have constitutive achlorhydia associated with a secondary elevation of serum gastrin levels. |
| 运输条件 | Dry Ice |
| 存放说明 | Store at -80C. Avoid freeze-thaw cycles. |
| 存储溶液 | Peptide dissolved in dH2O. Contains no BSA. |
| 浓度 | 1.0 mg/ml |
